August 2021 | Case of the Month

History

A 52 year old man presented with a one year history of skin lesions predominantly on his hands, ears and scalp. He was also complaining of painful swollen fingers associated with morning stiffness. There was no family history of skin or joint problems. 


Examination

Non-tender firm papules and nodules mainly on the backs of the hands and ears. There was joint deformity especially of the distal IP joints. 


Investigations

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Diagnosis

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Except for raised inflammatory markers, other blood tests were normal. A hand X-ray showed a destructive arthropathy. 

The diagnosis is multicentric reticulohistiocytosis, a rare histiocytic proliferative disorder, first described in 1954 by Goltz and Laymon, in which joints, skin and mucous membranes are affected. Other organs may be involved and 20% of patients have an internal malignancy.

For more information refer to the chapter multicentric reticulohistiocytosis. 

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